UMEM Educational Pearls

Category: Pediatrics

Title: Bechet Disease

Posted: 12/30/2011 by Rose Chasm, MD (Updated: 6/13/2024)
Click here to contact Rose Chasm, MD

  • vasculitis of small vessels with neutrophilic infiltration of venules and arterioles
  • classic triad:  painful recurrent oral and genital ulcers with inflammatory eye disease
  • key finding of recurrent buccal apthous ulcers (nearly 100% of patients)
  • diagnosis is made when recurrence of oral ulceration occurs at least 3 times in 1 year plus 2 of the following: recurrent genital ulceration , eye lesions, skin lesions, or positive pathergy test.
  • initial ED treatment is corticosteroids (oral or topical).  Reserve colchicine and pentoxifylline for ulcerative maifestations.

References

Pediatrics Board Review, MedStudy